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<article xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xmlns:ali="http://www.niso.org/schemas/ali/1.0/" article-type="other" dtd-version="1.2" xml:lang="en"><front><journal-meta><journal-id journal-id-type="publisher-id">Bone and soft tissue sarcomas, tumors of the skin</journal-id><journal-title-group><journal-title xml:lang="en">Bone and soft tissue sarcomas, tumors of the skin</journal-title><trans-title-group xml:lang="ru"><trans-title>Саркомы костей, мягких тканей и опухоли кожи</trans-title></trans-title-group></journal-title-group><issn publication-format="print">2219-4614</issn><issn publication-format="electronic">2782-3687</issn><publisher><publisher-name xml:lang="en">Publishing House ABV Press</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="publisher-id">30</article-id><article-categories><subj-group subj-group-type="toc-heading" xml:lang="en"><subject>SOFT TISSUE SARCOMAS</subject></subj-group><subj-group subj-group-type="toc-heading" xml:lang="ru"><subject>САРКОМЫ МЯГКИХ ТКАНЕЙ</subject></subj-group><subj-group subj-group-type="article-type"><subject></subject></subj-group></article-categories><title-group><article-title xml:lang="en">Extrarenal rhabdoid tumors in children. Case report</article-title><trans-title-group xml:lang="ru"><trans-title>Экстраренальные рабдоидные опухоли у детей. Случай из практики</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Khestanov</surname><given-names>D. B.</given-names></name><name xml:lang="ru"><surname>Хестанов</surname><given-names>Д. Б.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><email>hestanov@mail.ru</email><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Romantsova</surname><given-names>O. A.</given-names></name><name xml:lang="ru"><surname>Романцова</surname><given-names>О. А.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Kochneva</surname><given-names>V. V.</given-names></name><name xml:lang="ru"><surname>Кочнева</surname><given-names>В. В.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Hayrulova</surname><given-names>V. V.</given-names></name><name xml:lang="ru"><surname>Хайрулова</surname><given-names>В. В.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Senzhapova</surname><given-names>E. R.</given-names></name><name xml:lang="ru"><surname>Сенжапова</surname><given-names>Э. Р.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Dzampaev</surname><given-names>A. Z.</given-names></name><name xml:lang="ru"><surname>Дзампаев</surname><given-names>А. З.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Fedenko</surname><given-names>A. A.</given-names></name><name xml:lang="ru"><surname>Феденко</surname><given-names>А. А.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib><contrib contrib-type="author"><name-alternatives><name xml:lang="en"><surname>Aliev</surname><given-names>M. D.</given-names></name><name xml:lang="ru"><surname>Алиев</surname><given-names>М. Д.</given-names></name></name-alternatives><address><country country="RU">Russian Federation</country></address><xref ref-type="aff" rid="aff1"/></contrib></contrib-group><aff-alternatives id="aff1"><aff><institution xml:lang="en">FGBU «National Medical Research Center of Oncology named after N.N. Blokhin» of the Ministry of Health of Russia</institution></aff><aff><institution xml:lang="ru">ФГБУ «НМИЦ онкологии им. Н.Н. Блохина» Минздрава России</institution></aff></aff-alternatives><pub-date date-type="pub" iso-8601-date="2018-05-16" publication-format="electronic"><day>16</day><month>05</month><year>2018</year></pub-date><volume>10</volume><issue>2</issue><issue-title xml:lang="en"/><issue-title xml:lang="ru"/><fpage>49</fpage><lpage>54</lpage><history><date date-type="received" iso-8601-date="2021-04-16"><day>16</day><month>04</month><year>2021</year></date></history><permissions><copyright-statement xml:lang="en">Copyright ©; 2018, Khestanov D.B., Romantsova O.A., Kochneva V.V., Hayrulova V.V., Senzhapova E.R., Dzampaev A.Z., Fedenko A.A., Aliev M.D.</copyright-statement><copyright-statement xml:lang="ru">Copyright ©; 2018, Хестанов Д.Б., Романцова О.А., Кочнева В.В., Хайрулова В.В., Сенжапова Э.Р., Дзампаев А.З., Феденко А.А., Алиев М.Д.</copyright-statement><copyright-year>2018</copyright-year><copyright-holder xml:lang="en">Khestanov D.B., Romantsova O.A., Kochneva V.V., Hayrulova V.V., Senzhapova E.R., Dzampaev A.Z., Fedenko A.A., Aliev M.D.</copyright-holder><copyright-holder xml:lang="ru">Хестанов Д.Б., Романцова О.А., Кочнева В.В., Хайрулова В.В., Сенжапова Э.Р., Дзампаев А.З., Феденко А.А., Алиев М.Д.</copyright-holder><ali:free_to_read xmlns:ali="http://www.niso.org/schemas/ali/1.0/"/><license><ali:license_ref xmlns:ali="http://www.niso.org/schemas/ali/1.0/">https://creativecommons.org/licenses/by/4.0</ali:license_ref></license></permissions><self-uri xlink:href="https://sarbon.abvpress.ru/jour/article/view/30">https://sarbon.abvpress.ru/jour/article/view/30</self-uri><abstract xml:lang="en"><p>The search for neoadjuvant chemotherapy in pediatric patients with rhabdoid tumors is under way. As illustrated by this case report, etoposide/ifosfamide combination could be used as neoadjuvant treatment for patient with rhabdoid tumor.</p></abstract><trans-abstract xml:lang="ru"><p>Продолжается поиск неоадъювантной химиотерапии у пациентов детского возраста с рабдоидными опухолями. На примере лечения данного пациента наряду с использованием антрациклиновых противоопухолевых препаратов возможно применение схемы этопозид/ифосфамид в неоадъювантном режиме у пациентов с рабдоидной опухолью.</p></trans-abstract><kwd-group xml:lang="en"><kwd>rhabdoid tumors</kwd><kwd>children</kwd><kwd>surgical treatment</kwd><kwd>chemotherapy</kwd><kwd>rare tumors</kwd><kwd>survival</kwd><kwd>soft tissue sarcoma</kwd></kwd-group><kwd-group xml:lang="ru"><kwd>рабдоидные опухоли</kwd><kwd>дети</kwd><kwd>хирургическое лечение</kwd><kwd>химиотерапия</kwd><kwd>редкие опухоли</kwd><kwd>выживаемость</kwd><kwd>саркомы мягких тканей</kwd></kwd-group></article-meta></front><body></body><back><ref-list><ref id="B1"><label>1.</label><mixed-citation>Ammerlaan AC, Ararou A, Houben MP, Baas F, Tijssen CC, Teepen JL, Wesseling P, Hulsebos TJ. Long-term survival and transmission of INI1-mutation via nonpenetrant males in a family with rhabdoid tumour predisposition syndrome. 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