Bone and soft tissue sarcomas, tumors of the skinBone and soft tissue sarcomas, tumors of the skinСаркомы костей, мягких тканей и опухоли кожи2219-46142782-3687Publishing House ABV Press375Pediatric OncologyПЕДИАТРИЧЕСКАЯ ОНКОЛОГИЯPEComa. Literature review and case reportПекомы. Обзор литературы и клиническое наблюдениеNechushkinaI. V.НечушкинаИ. В.
Russian Federation

Moscow

г. Москва

KarseladzeA. I.КарселадзеА. И.
Russian Federation

Moscow

г. Москва

Pediatric Oncology & Hematology Research institute, N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russian FederationНИИ детской онкологии и гематологии ФГБУ «РОНЦ им. Н.Н. Блохина Минздрава РоссииClinical Oncology Research institute, N.N. Blokhin Russian Cancer Research Center, Ministry of Health of Russian FederationНИИ клинической онкологии ФГБУ «РОНЦ им. Н.Н. Блохина Минздрава России220420168232432201202222012022Copyright ©; 2016, Nechushkina I.V., Karseladze A.I.Copyright ©; 2016, Нечушкина И.В., Карселадзе А.И.2016Nechushkina I.V., Karseladze A.I.Нечушкина И.В., Карселадзе А.И.https://creativecommons.org/licenses/by/4.0https://sarbon.abvpress.ru/jour/article/view/375

The family of mesenchymal tumors called PEComas (Perivascular Epithelioid Cell Tumors) has been included in the international Classification of Soft Tissue and Bone Tumors since 2002. Literature review confirms difficulties of timely diagnosis and absence of progress in the treatment results. in spite of advances in research of PEComas histological nature of these tumors is still unclear. Further research of prognostic factors is needed to give proper treatment. Patients with PEComas of different primary sites require close follow-up after the treatment irrespective of malignant potential of tumors, as late recurrence and metastases are possible. This paper presents a case report of 11-year-old girl with vaginal PEComa, who is disease-free 10 years after the treatment.

С 2002 г. в международной классификации опухолей мягких тканей и костей выделено семейство мезенхимальных опухолей, обозначенных общим термином «пекомы» (PEComas). обзор литературных данных подтверждает трудности своевременной диагностики и отсутствие существенного прогресса в лечении больных. несмотря на достижения в области изучения пеком, гистологическая природа этих неоплазий до сих пор остается неясной. требуется дальнейшее изучение прогностических факторов для проведения адекватного лечения. больные, получившие лечение по поводу пеком различных локализаций, требуют тщательного динамического наблюдения независимо от потенциала опухоли, так как возможно развитие поздних рецидивов и метастазов. В статье представлены данные о лечении девочки 11 лет с пекомой влагалища и последующем наблюдении в течение 10 лет без признаков прогрессирования заболевания.

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